Accueil Recherches scientifique Publications scientifiques Meunier S et al : Severe haemorrhages leading to a diagnosis of rare bleeding disorder occur at a very young age. A study from the FranceCoag network Haemophilia

Publié le 12 juillet 2024

Meunier S et al : Severe haemorrhages leading to a diagnosis of rare bleeding disorder occur at a very young age. A study from the FranceCoag network Haemophilia

https://pubmed.ncbi.nlm.nih.gov/38738973/

PMID: 38738973
DOI: 10.1111/hae.15033

Abstract

In the context of severe unexplained haemorrhage (SH), it is usual to seek haematological evaluation and investigate for an inherited rare bleeding disorder (IRBD). In such circumstances, appropriate screen can discriminate between IRBD and suspected child abuse. Yet, little information is available about the frequency of SH in the population of patients with IRBD.

Keywords: central nervous system; constitutional haemorrhagic disease; haemophilia; registry; severe haemorrhage; von Willebrand disease.

© 2024 The Authors. Haemophilia published by John Wiley & Sons Ltd.

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