{"id":566,"date":"2024-01-14T21:05:26","date_gmt":"2024-01-14T20:05:26","guid":{"rendered":"https:\/\/www.francecoag.org\/presentation-of-france-coag\/project-francecoag\/target-population\/"},"modified":"2024-01-28T19:19:34","modified_gmt":"2024-01-28T18:19:34","slug":"target-population","status":"publish","type":"page","link":"https:\/\/www.francecoag.org\/en\/project-francecoag\/target-population\/","title":{"rendered":"Target population"},"content":{"rendered":"<p>The diseases eligible for the FranceCoag scheme are haemophilia, severe forms of rare HCM caused by another inherited coagulation protein deficiency (HCPD: afibrinogenemia, FII, FV, FVII, FX, FXI and FXIII deficiencies, FV+VIII, combined vitamin K-dependent factor deficiencies), symptomatic forms of Willebrand&#8217;s disease (WM) and inherited platelet diseases.<\/p>\n<p>The rate of monitoring and the size of the populations monitored are described in the table below. The FC acts as a registry for the most severe pathologies, i.e. :<\/p>\n<ol>\n<li>FVIII and FIX deficiencies with levels \u2264 5% (severe or moderate haemophilia A and B, including Leyden B forms with FIX \u2264 5%);<\/li>\n<li>the most severe forms of WM with a Willebrand Factor activity level (vWF:Act) \u2264 15% or an FVIII level \u2264 5% ;<\/li>\n<li>congenital afibrinogenemia with a fibrinogen level &lt; of 0.2 g\/l ;<\/li>\n<li>FXIII deficiency with an &lt; rate of 10% ;<\/li>\n<li>Glanzmann thrombasthenia (TG);<\/li>\n<li>Jean Bernard Soulier syndromes (SBS) ;<\/li>\n<li>other registrable platelet diseases.<\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>The diseases eligible for the FranceCoag scheme are haemophilia, severe forms of rare HCM caused by another inherited coagulation protein [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":565,"menu_order":6,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"class_list":["post-566","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.5 - 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